In what disease consists?
Malformation the Dandy-Walker – congenital anomaly of
development of a brain – is more true, one of its areas – areas IV zheludochka.
Particularly in Vanya a case
the basic misfortune consists in full absence of a worm of a cerebellum – the
body entering into system of regulation of movements.
This zone of a cerebellum to the
greatest degree is responsible for management of a muscular tone, a pose and
balance of a body. The information on position of a body in space and a
condition of the support-impellent device of a body there acts. This
information is processed in a bark of a cerebellum, the commands correcting
position of a body whence are transferred. Thus, absence of a worm of a
cerebellum creates impossibility of management of position of a body in space
– that the body of the person absolutely fine and can be normally developed
physically, the person not in a condition to stand, go, coordinate the
movements.
One more danger malformation
the Dandy-Walker consists in development of a hydrocephaly.
The term "hydrocephaly" in exact
translation means « head vodyanka
». This superfluous congestion of a spinal liquid in a cavity of a skull.
The substance head and a spinal
cord from different directions is constantly washed by a spinal liquid – likvorom. It
is transparent, a liquid feeding and protecting a brain.
In norm formation and
absorbability likvora
are in balance, the quantity of a liquid is constant, and accordingly,
pressure likvora
in a skull too is constant. But if functions of formation and imbibe are
broken, pressure inside of a skull will increase. Increase of intracranial
pressure is very dangerous, because the brain starts to be squeezed by the
accumulated superfluous liquid. At squeeze a brain the vital functions of an
organism, down to infringement of blood circulation and breath are broken.
Besides from squeeze brain blood circulation that leads to spasms and various
neurology infringements – parezam,
to paralyses, etc. If intracranial pressure will continue to increase vessels
of eyes are squeezed also that can lead to full blindness as a result is
broken also.
Till that time while at the child
were not closed rodnichki,
increase of intracranial pressure is partially compensated them vybukhaniem.
But after them zarastaniya
the skull turns to the closed vessel in which pressure progressively
increases, causing heavy consequences.
All aforesaid of is twice heavy
that Vanya intelligence will appear not broken and everything, that will
happen to him, he will realize completely. Imagine the human life, being in
full consciousness, sensible mind and firm memory, but not having
opportunities to operate the body! Any of us will come in horror at an idea
to be completely paralyses and dependent in all from another's hands, cannot
even independently take advantage of the spoon, a handkerchief, a toilet.
If to not help Vanya today,
him life it will appear almost same.
But
position can appear even more hard – increase of a hypostasis of a brain without
treatment is capable to lead to death.
Among possible heavy late
complications Vanya of disease is also siringomieliya - chronic
progressing disease of nervous system at which cavities in a chest department
of a spinal cord are formed, in an oblong brain and other departments of a
brain. Siringomieliya leads
to an atrophy of bones of the top part of a trunk and hands and to loss of
calcium curvature of bones and crises, heavy inflammatory processes in a
skin, an atrophy of muscles of hands by them is causes. In case of
insufficient treatment siringomieliya can
arise at teenage age.
The mainstream of treatment malformation
the Dandy-Walker consists in not admitting occurrence of heavy consequences
of a hydrocephaly. The basic struggle against a hypostasis of a brain is
spent by shunting – the operation consisting imposing kateter (a
tube allocating surplus likvora
from a cavity of a skull). Except for most kateter, the system includes also the
valve overlapping outflow of a liquid at normalization of intracranial
pressure that it did not fall below norm. As Vanya will grow, the shunt will appear
it is necessary periodically (approximately time in two years) to replace on
corresponding the sizes of a body. Behind shunting system regular supervision
as infringement of her functioning can lead to heavy consequences – down to a
fatal outcome in case of full refusal of system is necessary.
Besides this, the medicament
treatment reducing intracranial pressure, reducing production likvora, and also
improving brain blood circulation and stimulating regenerative processes in
fabrics of a brain steals up also.
It is known, that compensation
abilities of a brain are significant. Functions of an absent part of a
cerebellum somewhat are capable to incur other departments. If from early age
to be engaged in development Vanya of impellent skills it will promote
formation in a brain of additional communications – so to say, « roundabout
ways » on which nervous impulses to the support-impellent device are
transferred. It is reached by the long and constant directed occupations by
physiotherapy exercises, specialized massage, electro stimulation of
muscles, etc.
All this is necessary for
one reason. Absence of a cerebellum causes change of a muscular tone,
therefore LFK,
massage and other are required, that development of muscles occurred
correctly, otherwise the raised tone razgibatelej will interfere with an
opportunity to make normal volume of movements.
Whether it is possible to
tell, what Vanya position is hopeless?
No, in no event!
At duly both adequate
treatment and constant medical supervision at Vanya there is all chances not
only to avoid heavy consequences of disease, but also to grow almost same
child, as well as his contemporaries, with one exception – he never can go
independently. For walking to him the support and if support there is nothing
– special adaptations will be always required. In all rest he will appear
absolutely usual, normal person, not the greater invalid, than any person
with the damaged foots.
But that his tomorrow became
such, today your help is required to him.
Help him, please!